What causes OEIS?
What is cloacal exstrophy (OEIS Syndrome)? Cloacal exstrophy, also known as OEIS Syndrome, occurs when a portion of the large intestine lies outside of the body, and on either side of it —and connected to it — are the two halves of the bladder.
What does OEIS syndrome stand for?
Cloacal exstrophy (OEIS Syndrome) is a rare and complicated condition that affects the lower abdominal wall structures of infants In utero, occurring in 1 out of 200,000 pregnancies and 1 in 400,000 live births. It is often diagnosed prenatally (before birth) by a fetal ultrasound and confirmed at the time of birth.
What causes cloacal exstrophy?
The bladder exstrophy-epispadias-cloacal exstrophy complex is caused by a developmental abnormality that occurs 4-5 weeks after conception in which the cloacal membrane is not replaced by tissue that will form the abdominal muscles. The underlying cause of this error in development is not known.
What is cloacal bladder?
A child with cloacal exstrophy is born with the bladder and a part of the intestines open to the outside. The bony pelvis is also split open like a book. In males the penis is either flat and short or sometimes split. In females the clitoris is split and there may be two vaginal openings.
What is exstrophy of the bladder?
What is Bladder Exstrophy? An abnormality of formation of the bladder and the bony pelvis. The bladder does not form into its normal round shape but instead is flattened and exposed on the abdominal wall. The pelvic bones are also widely separated.
Is cloacal exstrophy genetic?
Both genetic and non-genetic causes are suspected. The medical literature has reported rare recurrences in subsequent pregnancies and cases of monozygotic (identical) twins who have both been born with cloacal exstrophy.
Can bladder exstrophy be cured?
Complete repair. This procedure is called complete primary repair of bladder exstrophy. Complete repair surgery is performed in a single procedure that closes the bladder and the abdomen and repairs the urethra and outer sex organs. This can be done soon after birth, or when the baby is around two to three months old.
Is cloacal exstrophy a disease?
It is a complex birth defect and requires a coordinated care plan developed with input from several specialists to assure the best outcomes. Cloacal exstrophy is at the most severe end of a spectrum of malformations called the Exstrophy- Epispadias Complex.
What is cloacal kiss?
SOME male birds possess a wiggling tongue-like knob on their genitals, probably to titillate their mates. In typical bird copulation, males and females momentarily press together their cloacas – genital openings – in what biologists call a cloacal kiss.
Which is worse omphalocele or gastroschisis?
18 Which has a worse prognosis, omphalocele or gastroschisis? Omphalocele has a worse prognosis because it is associated with a significantly increased incidence of chromosomal abnormalities (approximately 12%). This is much greater with omphaloceles that contain only bowel.